Amedco - Quiz

2019 MOC Single Topic Symposium


A   - Mustard-colored stools
B   - Normal gamma-glutamyl transferase levels (<200 U/L)
C   - Serum conjugated bilirubin of 0.2 mg/dL
D   - Normal aspartate and alanine aminotransferase levels
E   - Normal appearing gall bladder

A   - Delayed diagnosis because many radiology departments require pre-treatment
B   - Abnormal in many infants who do not have biliary atresia
C   - Normal in infants who have biliary atresia
D   - A and B

A   - Single gene testing
B   - Multi-gene test panel
C   - Whole exome sequencing
D   - Whole genome sequencing

A   - We have an answer—your child’s cholestasis is due to multiple gene variants
B   - We have a partial answer, start ursodeoxycholic acid
C   - The results from the gene panel do not currently explain your child’s cholestasis
D   - Reflex to whole exome sequencing
E   - Either c or d

A   - Hepatocellular carcinoma
B   - Hemangioma
C   - Hepatic cyst
D   - Hepatoblastoma
E   - Focal nodular hyperplasia

A   - NASH
B   - Acute liver failure due to viral hepatitis
C   - Congenital portosystemic shunt
D   - Budd-Chiari syndrome
E   - Portal vein thrombosis

A   - give a second dose of vitamin K intravenously.
B   - fresh frozen plasma intravenously.
C   - recombinant Factor VII intravenously.
D   - monitor for bleeding without intervening.

A   - Vitamin E 800 IU daily
B   - Metformin 1000 mg daily
C   - Lifestyle changes (diet and exercise)
D   - Obeticholic acid 25 mg daily

A   - Resolution of NASH, independent of fibrosis outcome
B   - Resolution of NASH without worsening of fibrosis
C   - Resolution of fibrosis, independent of NASH outcome
D   - Resolution of steatosis, independent of inflammation outcome

A   - Liver Transplantation
B   - Splenectomy
C   - Distal splenorenal shunt
D   - Transjugular intrahepatic portosystemic shunt

A   - Restoration of portal blood flow improves neurocognitive condition
B   - Improved flow assures patency
C   - Decreased occurrence of stenosis
D   - Worsens portal biliopathy

A   - Obtain a venous ammonia value with his next laboratory draw.
B   - Empirically start him on lactulose and reassess the report of his school performance in 4 months.
C   - Arrange for neuro psychological testing.
D   - Obtain cross-sectional abdominal imaging with contrast to look for spontaneous portosystemic shunts.

A   - Hepatic artery thrombosis
B   - ABO-incompatible liver transplantation
C   - Prolonged cold ischemia time
D   - EBV infection
E   - Older donor age

A   - Comparable to healthy children at one year post transplant.
B   - Not impacted by length of hospitalization.
C   - Is lower in patients with growth impairment at the time of transplant.
D   - Is not related to primary disease.

A   - Lowest in patient who have survived transplant by 5 years.
B   - Is approximately 30% in the first year following transplantation.
C   - Most likely due to pneumococcal infection.
D   - Most likely due to a gram negative infection.